Please confirm topic selection

Are you sure you want to trigger topic in your Anconeus AI algorithm?

Please confirm action

You are done for today with this topic.

Would you like to start learning session with this topic items scheduled for future?

Review Question - QID 102775

In scope icon M 5 D
QID 102775 (Type "102775" in App Search)
During the exam of a 2-day-old female neonate you determine that she appears lethargic, cyanotic, and has a coarse tremor of her right arm. The patient's mother explains that she observed what she believed to be seizure-like activity just before you arrived in the room. The mother has a history of type two diabetes mellitus and during childbirth there was a delay in cord clamping. You decide to get electrolytes and a complete blood count to work up this patient. The labs are significant for mild hypoglycemia and a hematocrit of 72%. What is the most effective treatment for this patient's condition?

Phlebotomy

0%

0/4

Partial exchange transfusion with hydration

75%

3/4

Fluid resuscitation

25%

1/4

Hydroxyurea

0%

0/4

Interferon alpha

0%

0/4

Select Answer to see Preferred Response

bookmode logo Review TC In New Tab

The baby presents with hemotcrit of 72% and clinical signs consistent with neonatal polycythemia rubra vera (p vera). The optimal treatment includes hydration and partial exchange transfusion (PET).

P vera of the newborn is defined as a hematocrit greater than 65%. Symptoms of p vera are related to hyperviscosity and include lethargy, cyanosis, tremors, seizures, apnea, respiratory distress, jitteriness, and irritability. This is more common in infants of diabetic mothers and instances of delayed cord clamping, twin-twin transfusion, Beckwith-Wiedemann syndrome, and excess placental transfusion. Treatment of neonatal p vera includes hydration and PET.

Dempsey et al. review PET as a treatment for neonatal hyperviscosity due to p vera. They acknowledge that the standard treatment for neonatal p vera is PET however, they question the long term benefits and outcomes attributed to PET treatment. They conclude that when deciding treatment for p vera in patients with minor symptoms or asymptomatic patients the provider should take into account the lack of evidence of the effectiveness of PET. However, studies have demonstrated benefit in patients with severe neurologic symptoms.

Sarkar et al. explain that polycythemia and hyperviscosity cause pathology by changing blood flow in specific organs. Although there is no data that supports the use of PET for treatment it continues to be used as treatment for symptomatic and asymptomatic neonates. Further, they explain that crystalloids are as effective as colloids for use in PET and should be used because of their lower cost and availability.

Incorrect Answers:
Answer 1: Phlebotomy is a possible treatment for adults with p vera but is not used for neonates.
Answer 3: Fluid resuscitation is part of the optimal treatment however, alone will not be enough to reduce the hematocrit to a safe level. Partial exchange transfusion is necessary to reduce the hematocrit to a safe level in the symptomatic neonate.
Answer 4: Hydroxyurea is used to treat adult p. vera NOT neonatal p vera. Hydroxyurea treats p. vera by reducing circulating platelets and red blood cells.
Answer 5: Interferon alpha is used to treat adult p. vera NOT neonatal p vera. Interferon alpha reduces bone marrow production of red blood cells.

REFERENCES (2)
Authors
Rating
Please Rate Question Quality

3.7

  • star icon star icon star icon
  • star icon star icon star icon
  • star icon star icon star icon
  • star icon star icon star icon
  • star icon star icon star icon

(3)

Attach Treatment Poll
Treatment poll is required to gain more useful feedback from members.
Please enter Question Text
Please enter at least 2 unique options
Please enter at least 2 unique options
Please enter at least 2 unique options